Fahr's syndrome. About a case

Authors

Keywords:

Fahr's syndrome, ferro-calcinosis, basal ganglia, dentate nuclei

Abstract

Fahr's syndrome, or cerebrovascular ferro-calcinosis, or calcinosis of the nuclei of the brain, is characterized by abnormal calcium deposition without abnormality in calcium metabolism. It accumulates mainly in the basal ganglia, cerebellar dentate nuclei and white matter. It is a degenerative neurological disorder associated with symptoms such as movement disorders and neuropsychiatric symptoms. The case of a 65-year-old male patient, from rural origin, widower, with a personal history of high blood pressure, type 1 diabetes mellitus, and prostate adenoma is presented. For this, he is treated with Cardicor, Lasix, Plaunac, DuoPlavin and Adenuric. He was taken to the emergency room by ambulance presenting generalized tonic-clonic seizures without sphincter relaxation, which responded to the administration of intravenous diazepam 10 mg. Fahr's syndrome was diagnosed, the patient progressed satisfactorily and was discharged 5 days after admission.

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Author Biographies

Alexander Durán-Flores, Hospital Tiberio Evoli di Melito di Porto Salvo. Reggio Calabria

Departamento de Emergencias

Lisbán Rodríguez-López, Policlínico Docente Hermanos Martínez Tamayo. Baracoa. Guantánamo

Departamento de Imagenología y Radiofísica Médica

Oneidis Durán-Flores, Hospital General Docente Octavio de la Concepción y la Pedraja. Baracoa. Guantánamo

Departamento de Anatomía Patológica

References

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Published

2024-05-08

How to Cite

1.
Durán-Flores A, Rodríguez-López L, Durán-Flores O. Fahr’s syndrome. About a case. Rev Méd Electrón [Internet]. 2024 May 8 [cited 2025 Jan. 23];46:e5420. Available from: https://revmedicaelectronica.sld.cu/index.php/rme/article/view/5420

Issue

Vol. 46 (2024)

Section

Presentation of cases

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