Periodical fever with aphthous stomatitis, pharyngitis, and adenitis (PFAPA syndrome)

Authors

  • Lázaro Arturo Vidal Tallet Hospital Pediátrico de Matanzas Eliseo Noel Caamaño. Matanzas.
  • Godetia Porto Álvarez Hospital Pediátrico de Matanzas Eliseo Noel Caamaño. Matanzas
  • Lianetzi Claro Moya Hospital Pediátrico de Matanzas Eliseo Noel Caamaño. Matanzas.
  • Oscar Antonio Montell Hernández Hospital Pediátrico de Matanzas Eliseo Noel Caamaño. Matanzas.
  • Belkis Rodríguez Rodríguez Hospital Pediátrico de Matanzas Eliseo Noel Caamaño. Matanzas.
  • Lidia Maria Díaz Estévez Hospital Pediátrico de Matanzas Eliseo Noel Caamaño. Matanzas.

Keywords:

fever, stomatitis, pharyngitis, adenitis

Abstract

 

We present a case of periodical fever with aphthous stomatitis, pharyngitis and adenitis (PFAPA syndrome), entity that is apparently infrequent and its report in the country was not found. Its etiology is not still clearly understood. It appears with higher frequency in the ages between 2 and 5 years, though it has been described in adult population. It is characterized by periodical fever with aphthous stomatitis, pharyngitis and adenitis of periodical character, with a dramatic answer to the use of steroids in most of the cases. The case that is presented is the one of a male patient aged 5 years with reiterative periodical fever associated to tonsillitis with exudate, adenitis and aphthous lesions, with answer, in the acute phase, to prednisone, and to cimetidine at the maintenance therapy. Nowadays, he is already 11 months in remission.

 

Downloads

Download data is not yet available.

Downloads

Published

2018-07-18

How to Cite

1.
Vidal Tallet LA, Porto Álvarez G, Claro Moya L, Montell Hernández OA, Rodríguez Rodríguez B, Díaz Estévez LM. Periodical fever with aphthous stomatitis, pharyngitis, and adenitis (PFAPA syndrome). Rev Méd Electrón [Internet]. 2018 Jul. 18 [cited 2025 Mar. 13];40(4):1179-85. Available from: https://revmedicaelectronica.sld.cu/index.php/rme/article/view/2381

Issue

Vol. 40 No. 4 (2018)

Section

Presentation of cases

License

All content published in this journal is Open Access, distributed under the terms of the CC BY-NC 4.0 License.

It allows:

 - Copy and redistribute published material in any medium or format.

 - Adapt the content.

 This will be done under the following terms:

 - Attribute the authors' credits and indicate whether changes were made, in which case it must be in a reasonable way.

 - Non-commercial use.

 - Recognize the journal where it is published.

 The copyrights of each article are maintained, without restrictions.