Characterization of patients with intracranial ependymoma in the pediatric hospital Juan Manuel Márquez. 2012-2017

Authors

Keywords:

brain tumor, intracranial ependymoma, pediatric.

Abstract

Introduction: ependymoma are almost 3-5 % of the intracranial tumors and 5-10 % of the brain tumors in pediatric age. Objective: to characterize the patients with intracranial ependymoma who underwent surgery in the Pediatric Hospital ¨Juan Manuel Márquez.¨
Materials and methods: retrospective, descriptive study of patients in pediatric age with histological diagnosis of ependymoma of intracranial location in the period January 2012-December 2017. The universe was formed by all patients of pediatric age who underwent surgery with histological diagnosis of intracranial ependymoma in the before-mentioned place and period (N=22).
Results: the average age was 2.75 years with limits between 1 and 17 years old. Male patients represented 63.64 %; the relation with female sex during the first 4 years was 1:1.  Regarding the clinical characteristics, hydrocephaly predominated in 72.73 % of patients. Intracranial ependymoma of infratentorial location (63.64 %) predominated. 45.45 % of the studied lesions corresponded to the histological subtype of anaplastic ependymoma.
Conclusions:the combination of surgery, radiotherapy and chemotherapy was used in most of the cases. The direct approach of the lesion through craniotomy and a removal adequate to ependymoma location predominated. However, in most of them just the resection of 50-90 % was achieved. The evolution of most of patients after the diagnosis evidenced a tendency to the stability.

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Published

2020-04-29

How to Cite

1.
Hernández Román G, Sierra Benitez EM, Infante Pérez M, Rodríguez Ramos E. Characterization of patients with intracranial ependymoma in the pediatric hospital Juan Manuel Márquez. 2012-2017. Rev Méd Electrón [Internet]. 2020 Apr. 29 [cited 2025 Jan. 10];42(3):1-13. Available from: https://revmedicaelectronica.sld.cu/index.php/rme/article/view/3324

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Research article

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