Solid cystic pseudo-papillary neoplasm of the pancreas: Frantz tumor

Authors

Keywords:

pancreas tumor, Franz tumor, pseudopapillary neoplasia of the pancreas

Abstract

Pseudopapillary tumors of the pancreas are rare; they comprise between 0.3 and 2.7% of all pancreatic tumors. Their etiology is still uncertain; however a hormonal origin is postulated, being more common in women in the third decade of life. The absence of symptoms, without metabolic changes, or elevation of biomarkers, means that imaging diagnosis is often incidental, which makes its diagnosis difficult. The objective is to describe the diagnostic system and the conduct taken, to review the state of the art and the related literature due to the infrequency of this entity. This is the case of a 51-year-old female patient who comes to consultation due to an incidental diagnosis of distal pancreatic tumor after a study for abdominal pain and long-turn dyspeptic disorders. Extension studies are carried out and corpocaudal pancreatectomy with splenectomy is performed as surgical treatment with good recovery. Frantz tumor is a rare entity and its symptoms are usually vague or absent. The case shown in this study has a presentation similar to that described in the reviewed literature in terms of clinical characteristics and diagnostic studies. The treatment is surgical in most cases and aims to radically resect the tumor.

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Author Biographies

Alberto Suárez-Cuevas, Instituto Nacional de Oncología y Radiobiología. La Habana

Especialista de segundo grado en Cirugía General Especialista de primer grado en Medicina General Integral Diplomado en Cirugía Oncológica Investigador Agregado Profesor Asistente

Rafael Isaia Reyes-Velázquez, Instituto Nacional de Oncología y Radiobiología. La Habana

Especialista de primer grado en Imagenologia y en Medicina General Integral. Máster en Procederes Diagnósticos Profesor Auxiliar

Olga Noemí Rodríguez-Marrero, Instituto Nacional de Oncología y Radiobiología. La Habana

Especialista de primer grado en Oncología Clínica y en Medicina General Integral Máster en Diseño y Conducción de Ensayos Clínicos Departamento de Ensayos Clínicos

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Published

2024-08-13

How to Cite

1.
Suárez-Cuevas A, Reyes-Velázquez RI, Rodríguez-Marrero ON. Solid cystic pseudo-papillary neoplasm of the pancreas: Frantz tumor. Rev Méd Electrón [Internet]. 2024 Aug. 13 [cited 2025 Jan. 15];46:e5676. Available from: https://revmedicaelectronica.sld.cu/index.php/rme/article/view/5676

Issue

Vol. 46 (2024)

Section

Presentation of cases

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